Porphyria
Alternate Names : Acute intermittent porphyria, Hereditary coproporphyria, Congenital erythropoietic porphyria, Erythropoietic protoporphyria
Treatment
Some of the medicines used to treat a sudden (acute) attack of porphyria may include: - Hematin given through a vein (intravenously)
- Pain medication
- Propranolol to control the heartbeat
- Sedatives to help you feel sleepy and less anxious
Other treatments may include:
- Chloroquine
- Fluids and glucose to boost carbohydrate levels, which helps limit the production of porphyrins
- Removal of blood (phlebotomy)
- Beta-carotene supplements
Depending on the type of porphyria you have, your doctor may tell you to: - Avoid all alcohol
- Avoid drugs that may trigger an attack
- Avoid injuring the skin
- Avoid sunlight as much as possible and use sunscreen when outside
- Eat a high-carbohydrate diet
Prognosis (Expectations)
Porphyrias are life-long diseases with symptoms that come and go. Some forms of the disease cause more symptoms than others. Proper treatment and avoidance of triggers can help reduce the time between attacks.
Complications
Calling Your Health Care Provider
Seek medical attention as soon as you have signs of an acute attack. Talk to your doctor about your risk for this condition if you have a long history of undiagnosed abdominal pain, muscle and nerve problems, and sensitivity to sunlight.
|