Multiple endocrine neoplasia (MEN) II
Alternate Names : Sipple's syndrome
Treatment
Surgery is needed to remove both the medullary carcinoma of the thyroid and the pheochromocytoma. For medullary carcinoma of the thyroid, the thyroid gland and surrounding lymph nodes must be totally removed. Thyroid hormone replacement therapy is given after surgery. Surgery to remove the thyroid before it becomes cancerous is often being performed at an early age (before age 5) in people with known MEN IIa, and before age 6 months in people with MEN IIb.
Family members should be screened for the RET gene mutation.
Prognosis (Expectations)
Pheochromocytoma is usually not cancerous (benign). Medullary carcinoma of the thyroid is a very aggressive and potentially fatal cancer. However, early diagnosis and surgery can often lead to a cure.
Complications
The spread of cancerous cells is a complication.
Calling Your Health Care Provider
Call your health care provider if you notice symptoms of MEN II.
|
Previous
