Neuronal Ceroid Lipofuscinoses (NCLS)
Alternate Names : Batten Disease, Jansky-Bielschowsky, Kufs' Disease, Lipofuscinoses, Spielmeyer-Vogt
Neuronal Ceroid Lipofuscinoses (NCLS): Complications
There is typically visual impairment or blindness in early onset forms of the disease. Mental impairment can range from severe retardation at birth to only late onset dementia. There can be severe problems with the nerves that control muscle tone resulting in rigidity. The person may become totally dependent on others for help with daily activities.
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