Hypertrophic cardiomyopathy
Alternate Names : Cardiomyopathy - hypertrophic (HCM), IHSS, Idiopathic hypertrophic subaortic stenosis, Asymmetric septal hypertrophy, ASH, HOCM, Hypertrophic obstructive cardiomyopathy
Treatment
The goal of treatment is to control symptoms and prevent complications. Some patients may need to stay in the hospital until the condition is under control (stabilized). If you have symptoms, you may need medication to help the heart contract and relax correctly. Drugs include beta-blockers and calcium channel blockers. These medicines reduce chest pain and pain during exercise. Medications will often relieve symptoms so patients do not need more invasive treatments.
Some people with arrhythmias may need anti-arrhythmic medications. If the arrhythmia is due to atrial fibrillation, blood thinners will also be used to reduce the risk of blood clots. Some patients may have a permanent pacemaker placed. However, pacemakers are used less often today than they were in the past. When blood flow out of the heart is severely blocked, an operation called surgical myectomy is done. This procedure cuts and removes the thickened part of the heart. Patients who have this procedure often show significant improvement. If the heart's mitral valve is leaking, surgery may be done to repair or replace the valve. In some cases, patients may be given an injection of alcohol into the arteries that feed the thickened part of the heart (alcohol septal ablation). An implantable-cardioverter defibrillator (ICD) may be needed to prevent sudden death. ICDs are used in high-risk patients. High risks include: - Drop in blood pressure during exercise
- Family history of cardiac arrest
- History of cardiac arrest or ventricular tachycardia
- History of unexplained fainting
- Life-threatening heart rhythms on a Holter monitor
- Severe heart muscle thickness
Prognosis (Expectations)
Some people with hypertrophic cardiomyopathy may not have symptoms and live a normal lifespan. Others may get worse over time or rapidly. The condition may develop into dilated cardiomyopathy in some patients. People with hypertrophic cardiomyopathy are at higher risk for sudden death than the normal population. Sudden death can occur at a young age. Hypertrophic cardiomyopathy is a well-known cause of sudden death in athletes. Almost half of deaths in hypertrophic cardiomyopathy happen during or just after the patient has done some type of physical activity. If you have hypertrophic cardiomyopathy, always follow your doctor's advice concerning exercise and medical appointments. Avoid strenuous exercise.
Complications
- Dilated cardiomyopathy
- Heart failure
- Life-threatening heart rhythm problems (arrhythmias)
- Severe injury from fainting
Calling Your Health Care Provider
Call for an appointment with your health care provider if: - You have any symptoms of hypertrophic cardiomyopathy
- You develop chest pain, palpitations, faintness, or other new or unexplained symptoms
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